Urea Cycle Disorder Agents
- Name
- Urea Cycle Disorder Agents
- Accession Number
- DBCAT002683
- Description
Not Available
- Drugs
Drug Drug Description Phenylbutyric acid An agent indicated for the adjunctive therapy for the management of chronic urea cycle disorders due to deficiencies in specific enzymes, including the neonatal-onset deficiency and late-onset disease with a history of hyperammonemic encephalopathy. Glycerol phenylbutyrate A nitrogen-binding agent used to manage patients with urea cycle disorders who cannot be sufficiently managed amino acid supplementation and/or dietary restrictions. Benzoic acid An antimicrobial food additive. Phenylacetic acid An agent used as an adjunct to treat acute hyperammonemia and associated encephalopathy in adult and pediatric patients with deficiencies in enzymes of the urea cycle. - Drugs & Drug Targets